Müllerian Agenesis and Beyond: A Comprehensive Analysis of Rokitansky-Küster-Hauser Syndrome

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Rebeca Álvarez Fernández
Abril Mariana Abraham Mexicano
Emmanuel Bautista Perea
Blanca Areni González Solís
Imanol Guadalupe Martínez
Luis Enrique Morales Montoya

Abstract

Rokitansky-Küster-Hauser syndrome (RKH), also known as Müllerian agenesis, represents a rare congenital disorder characterized by the absence or underdevelopment of the müllerian duct structures in phenotypic females. This condition manifests as primary amenorrhea, with a typical constellation of associated anomalies encompassing the urogenital and skeletal systems. Despite its rarity, RKH poses significant physical, psychological, and reproductive challenges to affected individuals. This comprehensive article endeavors to elucidate the complex clinical spectrum, pathogenesis, diagnostic modalities, and multidisciplinary management strategies for Rokitansky-Küster-Hauser syndrome.

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How to Cite
Rebeca Álvarez Fernández, Abril Mariana Abraham Mexicano, Emmanuel Bautista Perea, Blanca Areni González Solís, Imanol Guadalupe Martínez, & Luis Enrique Morales Montoya. (2023). Müllerian Agenesis and Beyond: A Comprehensive Analysis of Rokitansky-Küster-Hauser Syndrome. International Journal of Medical Science and Clinical Research Studies, 3(10), 2410–2415. https://doi.org/10.47191/ijmscrs/v3-i10-56
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Articles

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